Publications

  1. Kindel SJ, Hsu HH, Hussain T, Johnson JN, McMahon CJ, Kutty S. Multimodality Noninvasive Imaging in the Monitoring of Pediatric Heart Transplantation. J Am Soc Echocardiogr. 2017 Sep; 30 (9):859-870
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  2. Putschoegl A, Dipchand AI, Ross H, Chaparro C, Johnson JN. Transitioning from pediatric to adult care after thoracic transplantation. J Heart Lung Transplant. 2017 Aug; 36 (8):823-829 Epub 2017 Feb 28
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  3. Kelle AM, Bos JM, Etheridge SP, Cannon BC, Bryant RM, Johnson JN, Ackerman MJ. Cardiac transplantation in children and adolescents with long QT syndrome. Heart Rhythm. 2017 Aug; 14 (8):1182-1188 Epub 2017 Apr 14
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  4. Johnson JN, Barrett CS, Franklin WH, Graham EM, Halnon NJ, Hattendorf BA, Krawczeski CD, McGovern JJ, O'Connor MJ, Schultz AH, Vinocur JM, Chowdhury D, Anderson JB. Development of quality metrics for ambulatory pediatric cardiology: Infection prevention. Congenit Heart Dis. 2017 Jul 25;
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  5. Niaz T, Poterucha JT, Johnson JN, Craviari C, Nienaber T, Palfreeman J, Cetta F, Hagler DJ. Incidence, morphology, and progression of bicuspid aortic valve in pediatric and young adult subjects with coexisting congenital heart defects. Congenit Heart Dis. 2017 May; 12: (3)261-269.
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  6. Hilscher MB, Johnson JN, Cetta F, Driscoll DJ, Poterucha JJ, Sanchez W, Connolly HM, Kamath PS. Surveillance for liver complications after the Fontan procedure. Congenit Heart Dis. 2017 Mar; 12 (2):124-132 Epub 2017 Jan 31
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  7. Chowdhury D, Gurvitz M, Marelli A, Anderson J, Baker-Smith C, Diab KA, Edwards TC, Hougen T, Jedeikin R, Johnson JN, Karpawich P, Lai W, Lu JC, Mitchell S, Newburger JW, Penny DJ, Portman MA, Satou G, Teitel D, Villafane J, Williams R, Jenkins K, American College of Cardiology's Adult Congenital and Pediatric Cardiology Section's Ambulatory Pediatric Cardiology Quality Metrics Working Group. Development of Quality Metrics in Ambulatory Pediatric Cardiology. J Am Coll Cardiol. 2017 Feb 07; 69: (5)541-555.
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  8. Poterucha JT, Taggart NW, Johnson JN, Cannon BC, Cabalka AK, Hagler DJ, Dearani JA, Cetta F. Intravascular and hybrid intraoperative stent placement for baffle obstruction in transposition of the great arteries after atrial switch. Catheter Cardiovasc Interv. 2017 Feb 01; 89: (2)306-314.
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  9. Pundi KN, Pundi KN, Johnson JN, Dearani JA, Li Z, Driscoll DJ, Wackel PL, McLeod CJ, Cetta F, Cannon BC. Sudden cardiac death and late arrhythmias after the Fontan operation. Congenit Heart Dis. 2017 Jan; 12: (1)17-23.
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  10. Poterucha JT, Egbe AC, Johnson JN, Niaz T, Wackel PL, Cannon BC, Eidem BW, Cetta F. Improved Ventricular Function after TEE-guided Cardioversion of Atrial Arrhythmias in Patients after the Fontan Operation. Congenit Heart Dis. 2016 Dec; 11: (6)578-583.
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  11. Pundi KN, Pundi K, Driscoll DJ, Dearani JA, Li Z, Dahl SH, Mora BN, O'Leary PW, Daly RC, Cetta F, Johnson JN. Heart transplantation after Fontan: Results from a surgical Fontan cohort. Pediatr Transplant. 2016 Dec; 20 (8):1087-1092 Epub 2016 July 10
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  12. Acheampong B, Johnson JN, Stulak JM, Dearani JA, Kushwaha SS, Daly RC, Haile DT, Schears GJ. Postcardiotomy ECMO Support after High-risk Operations in Adult Congenital Heart Disease. Congenit Heart Dis. 2016 Dec; 11: (6)751-755.
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  13. Egbe AC, Connolly HM, Dearani JA, Bonnichsen CR, Niaz T, Allison TG, Johnson JN, Poterucha JT, Said SM, Ammash NM. When is the right time for Fontan conversion? The role of cardiopulmonary exercise test. Int J Cardiol. 2016 Oct 01; 220:564-8.
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  14. Sessions KL, Anderson JH, Johnson JN, Taggart NW. AngioJet thrombolysis of SVC thrombosis after orthotopic heart transplantation: A case report. Pediatr Transplant. 2016 Aug; 20: (5)723-726.
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  15. Pundi K, Pundi K, Kamath PS, Cetta F, Li Z, Poterucha JT, Driscoll DJ, Johnson JN. Liver Disease in Patients After the Fontan Operation. Am J Cardiol. 2016 Feb 1; 117: (3)456-60.
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  16. Anderson HN, Burkhart HM, Johnson JN. Septal myectomy for hypertrophic obstructive cardiomyopathy in Friedreich's ataxia. Cardiol Young. 2016 Jan; 26: (1)175-8.
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  17. Pundi KN, Johnson JN, Dearani JA, Bonnichsen CR, Phillips SD, Canobbio MC, Driscoll DJ, Cetta F. Contraception Practices and Pregnancy Outcome in Patients after Fontan Operation. Congenit Heart Dis. 2016 Jan-Feb; 11: (1)63-70.
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  18. Thompson AJ, Cannon BC, Wackel PL, Horner JM, Ackerman MJ, O'Leary PW, Eidem BW, Johnson JN. Electrocardiographic abnormalities in elite high school athletes: comparison to adolescent hypertrophic cardiomyopathy. Br J Sports Med. 2016 Jan; 50: (2)105-10.
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  19. Meeusen JW, Johnson JN, Gray A, Wendt P, Jefferies JL, Jaffe AS, Donato LJ, Saenger AK. Soluble ST2 and galectin-3 in pediatric patients without heart failure. Clin Biochem. 2015 Dec; 48: (18)1337-40.
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  20. Pundi KN, Johnson JN, Dearani JA, Pundi KN, Li Z, Hinck CA, Dahl SH, Cannon BC, O'Leary PW, Driscoll DJ, Cetta F. 40-Year Follow-Up After the Fontan Operation: Long-Term Outcomes of 1,052 Patients. J Am Coll Cardiol. 2015 Oct 13; 66: (15)1700-10.
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  21. Poterucha JT, Johnson JN, O'Leary PW, Connolly HM, Niaz T, Maleszewski JJ, Ackerman MJ, Cetta F, Dearani JA, Eidem BW. Surgical Ventricular Septal Myectomy for Patients With Noonan Syndrome and Symptomatic Left Ventricular Outflow Tract Obstruction. Am J Cardiol. 2015 Oct 01; 116: (7)1116-21.
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  22. Poterucha JT, Johnson JN, Taggart NW, Cabalka AK, Hagler DJ, Driscoll DJ, Cetta F. Embolization of Veno-venous Collaterals after the Fontan Operation Is Associated with Decreased Survival. Congenit Heart Dis. 2015 Sep-Oct; 10: (5)E230-6.
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  23. Poterucha JT, Johnson JN, Qureshi MY, O'Leary PW, Kamath PS, Lennon RJ, Bonnichsen CR, Young PM, Venkatesh SK, Ehman RL, Gupta S, Smyrk TC, Dearani JA, Warnes CA, Cetta F. Magnetic Resonance Elastography: A Novel Technique for the Detection of Hepatic Fibrosis and Hepatocellular Carcinoma After the Fontan Operation. Mayo Clin Proc. 2015 Jul; 90: (7)882-94.
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  24. Quintana E, Johnson JN, Sabate Rotes A, Cetta F, Ommen SR, Schaff HV, Dearani JA. Surgery for biventricular obstruction in hypertrophic cardiomyopathy in children and young adults: technique and outcomesdagger. Eur J Cardiothorac Surg. 2015 Jun; 47: (6)1006-12.
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  25. Sabate Rotes A, Johnson JN, Burkhart HM, Eidem BW, Allison TG, Driscoll DJ. Cardiorespiratory Response to Exercise before and after Pulmonary Valve Replacement in Patients with Repaired Tetralogy of Fallot: A Retrospective Study and Systematic Review of the Literature. Congenit Heart Dis. 2015 May-Jun; 10: (3)263-70.
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  26. Johnson JN, Ackerman MJ, Cannon BC. Atypical atrioventricular nodal reentry tachycardia in a child with polyvalvular dysplasia. Cardiol Young. 2015 Mar; 25(3):584-7. Epub 2014 May 09.
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  27. Medford BA, Taggart NW, Cabalka AK, Cetta F, Reeder GS, Hagler DJ, Johnson JN. Intracardiac echocardiography during atrial septal defect and patent foramen ovale device closure in pediatric and adolescent patients. J Am Soc Echocardiogr. 2014 Sep; 27: (9)984-90.
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  28. Said SM, Burkhart HM, Schaff HV, Johnson JN, Connolly HM, Dearani JA. When should a mechanical tricuspid valve replacement be considered? J Thorac Cardiovasc Surg. 2014 Aug; 148(2):603-8. Epub 2013 Nov 04.
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  29. Raju V, Dearani JA, Burkhart HM, Grogan M, Phillips SD, Ammash N, Pike RP, Johnson JN, O'Leary PW. Right ventricular unloading for heart failure related to Ebstein malformation. Ann Thorac Surg. 2014 Jul; 98(1):167-73; discussion 173-4. Epub 2014 May 6
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  30. Schneider AE, Johnson JN, Taggart NW, Cabalka AK, Hagler DJ, Reeder GS, Cetta F. Percutaneous coronary intervention in pediatric and adolescent patients. Congenit Heart Dis. 2014 May-Jun; 9(3):228-34. Epub 2013 Aug 15
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  31. Flores S, Johnson J, Young P, Tollefson M. Boy with yellow-orange, rough nodule on right thigh. JAMA Pediatr. 2014 May; 168(5):493-4.
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  32. Gossl M, Johnson JN, Hagler DJ. Failing left ventricle to ascending aorta conduit-Hybrid implantation of a melody valve and NuMed covered stent. Catheter Cardiovasc Interv. 2014 Apr 1; 83(5):778-81. Epub 2013 Nov 18
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  33. Robinson JA, Driscoll DJ, O'Leary PW, Burkhart HM, Dearani JA, Daly RC, Edwards BS, Dahl SH, Johnson JN. Cardiac and multiorgan transplantation for end-stage congenital heart disease. Mayo Clin Proc. 2014 Apr; 89(4):478-83.
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  34. Craviari C, Taggart NW, Cetta F, Hagler DJ, Bower TC, Mauriello DA, Johnson JN. Percutaneous treatment of a complex saccular aortic pseudoaneurysm with covered stenting after subclavian artery translocation. JACC Cardiovasc Interv. 2014 Mar; 7(3):e23-4.
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  35. Loar RW, Driscoll DJ, Kushwaha SS, Cramer CH, O'Leary PW, Daly RC, Mauriello DA, Johnson JN. Empiric switch from calcineurin inhibitor to sirolimus-based immunosuppression in pediatric heart transplantation recipients. Pediatr Transplant. 2013 Dec; 17(8):794-9. Epub 2013 Oct 06.
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  36. Bos JM, Bos KM, Johnson JN, Moir C, Ackerman MJ. Left cardiac sympathetic denervation in long QT syndrome: analysis of therapeutic nonresponders. Circ Arrhythm Electrophysiol. 2013 Aug; 6(4):705-11. Epub 2013 May 31.
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  37. Sriram CS, Syed FF, Ferguson ME, Johnson JN, Enriquez-Sarano M, Cetta F, Cannon BC, Asirvatham SJ, Ackerman MJ. Malignant bileaflet mitral valve prolapse syndrome in patients with otherwise idiopathic out-of-hospital cardiac arrest. J Am Coll Cardiol. 2013 Jul 16; 62(3):222-30. Epub 2013 Apr 03.
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  38. Haugaa KH, Johnson JN, Bos JM, Phillips BL, Eidem BW, Ackerman MJ. Subclinical cardiomyopathy and long QT syndrome: an echocardiographic observation. Congenit Heart Dis. 2013 Jul-Aug; 8: (4)352-9.
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  39. Loar RW, Johnson JN, Cabalka AK, Cetta F, Hagler DJ, Eidem BW, Taggart NW. Effect of percutaneous atrial septal defect and patent foramen ovale device closure on degree of aortic regurgitation. Catheter Cardiovasc Interv. 2013 Jun 01; 81: (7)1234-7.
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  40. Bartos DC, Anderson JB, Bastiaenen R, Johnson JN, Gollob MH, Tester DJ, Burgess DE, Homfray T, Behr ER, Ackerman MJ, Guicheney P, Delisle BP. A KCNQ1 mutation causes a high penetrance for familial atrial fibrillation. J Cardiovasc Electrophysiol. 2013 May; 24(5):562-9. Epub 2013 Jan 25.
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  41. Loar RW, Patterson MC, O'Leary PW, Driscoll DJ, Johnson JN. Posterior reversible encephalopathy syndrome and hemorrhage associated with tacrolimus in a pediatric heart transplantation recipient. Pediatr Transplant. 2013 Mar; 17(2):E67-70. Epub 2013 Jan 17.
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  42. Bowman J, Johnson J, McKusick M, Gloviczki P, Driscoll D. Outcomes of sclerotherapy and embolization for arteriovenous and venous malformations. Semin Vasc Surg. 2013 Mar; 26(1):48-54.
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  43. Johnson JN, Kvistad BS, Reed AM, Porter CB, O'Leary PW, Driscoll DJ. Cardiac transplantation in a pediatric patient with systemic sclerosis. Congenit Heart Dis. 2013 Jan-Feb; 8: (1)E1-4.
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  44. Johnson JN, Ackerman MJ. Return to play? Athletes with congenital long QT syndrome. Br J Sports Med. 2013 Jan; 47(1):28-33. Epub 2012 Nov 28.
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  45. Chockalingam P, Crotti L, Girardengo G, Johnson JN, Harris KM, van der Heijden JF, Hauer RN, Beckmann BM, Spazzolini C, Rordorf R, Rydberg A, Clur SA, Fischer M, van den Heuvel F, Kaab S, Blom NA, Ackerman MJ, Schwartz PJ, Wilde AA. Not all beta-blockers are equal in the management of long QT syndrome types 1 and 2: higher recurrence of events under metoprolol. J Am Coll Cardiol. 2012 Nov 13; 60(20):2092-9. Epub 2012 Oct 17
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  46. Burgess DE, Bartos DC, Reloj AR, Campbell KS, Johnson JN, Tester DJ, Ackerman MJ, Fressart V, Denjoy I, Guicheney P, Moss AJ, Ohno S, Horie M, Delisle BP. High-risk long QT syndrome mutations in the Kv7.1 (KCNQ1) pore disrupt the molecular basis for rapid K(+) permeation. Biochemistry. 2012 Nov 13; 51(45):9076-85. Epub 2012 Nov 02.
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  47. Johnson JN, Ackerman MJ. Competitive sports participation in athletes with congenital long QT syndrome. JAMA. 2012 Aug 22; 308: (8)764-5.
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  48. Coleman MA, Bos JM, Johnson JN, Owen HJ, Deschamps C, Moir C, Ackerman MJ. Videoscopic left cardiac sympathetic denervation for patients with recurrent ventricular fibrillation/malignant ventricular arrhythmia syndromes besides congenital long-QT syndrome. Circ Arrhythm Electrophysiol. 2012 Aug 1; 5: (4)782-8.
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  49. Johnson JA, Boyce TG, Cetta F, Steckelberg JM, Johnson JN. Infective endocarditis in the pediatric patient: a 60-year single-institution review. Mayo Clin Proc. 2012 Jul; 87(7):629-35.
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  50. Johnson JN, Driscoll DJ, O'Leary PW. Protein-losing enteropathy and the Fontan operation. Nutr Clin Pract. 2012 Jun; 27(3):375-84. Epub 2012 Apr 19.
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  51. Van Dorn CS, Johnson JN, Taggart NW, Thorkelson L, Ackerman MJ. QTc values among children and adolescents presenting to the emergency department. Pediatrics. 2011 Dec; 128: (6)e1395-401.
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  52. Johnson JN, Harris KM, Moir C, Lau YR, Ackerman MJ. Left cardiac sympathetic denervation in a pediatric patient with hypertrophic cardiomyopathy and recurrent ventricular fibrillation. Heart Rhythm. 2011 Oct; 8: (10)1591-4.
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  53. Johnson JN, Bonnichsen CR, Julsrud PR, Burkhart HM, Hagler DJ. Single coronary artery giving rise to an intraseptal left coronary artery in a patient presenting with neurocardiogenic syncope. Cardiol Young. 2011 Oct; 21(5):572-6. Epub 2011 May 23.
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  54. Mauriello DA, Johnson JN, Ackerman MJ. Holter monitoring in the evaluation of congenital long QT syndrome. Pacing Clin Electrophysiol. 2011 Sep; 34(9):1100-4. Epub 2011 Apr 20.
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  55. Johnson JN, Marquardt ML, Ackerman MJ, Asirvatham SJ, Reeder GS, Cabalka AK, Cetta F, Hagler DJ. Electrocardiographic changes and arrhythmias following percutaneous atrial septal defect and patent foramen ovale device closure. Catheter Cardiovasc Interv. 2011 Aug 1; 78(2):254-61. Epub 2011 May 11.
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  56. Moseley BD, Wirrell EC, Nickels K, Johnson JN, Ackerman MJ, Britton J. Electrocardiographic and oximetric changes during partial complex and generalized seizures. Epilepsy Res. 2011 Aug; 95(3):237-45. Epub 2011 May 10
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  57. Johnson JN, Grifoni C, Bos JM, Saber-Ayad M, Ommen SR, Nistri S, Cecchi F, Olivotto I, Ackerman MJ. Prevalence and clinical correlates of QT prolongation in patients with hypertrophic cardiomyopathy. Eur Heart J. 2011 May; 32: (9)1114-20.
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  58. Johnson JN, Ackerman MJ. The prevalence and diagnosticprognostic utility of sinus arrhythmia in the evaluation of congenital long QT syndrome. Heart Rhythm. 2010 Dec; 7: (12)1785-9.
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  59. Johnson JN, Driscoll DJ, McGregor CG. Pulmonary thromboendarterectomy in Klippel-Trenaunay syndrome. J Thorac Cardiovasc Surg. 2010 Sep; 140(3):e41-3.
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  60. Johnson JN, Tester DJ, Bass NE, Ackerman MJ. Cardiac channel molecular autopsy for sudden unexpected death in epilepsy. J Child Neurol. 2010 Jul; 25: (7)916-21.
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  61. Johnson JN, Driscoll DJ, McGregor CG. Pulmonary thromboendarterectomy in adolescents and young adults. Pediatr Pulmonol. 2010 Jun; 45(6):614-8.
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  62. Mack KJ, Johnson JN, Rowe PC. Orthostatic intolerance and the headache patient. Semin Pediatr Neurol. 2010 Jun; 17(2):109-16.
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  63. Johnson JN, Mack KJ, Kuntz NL, Brands CK, Porter CJ, Fischer PR. Postural orthostatic tachycardia syndrome: a clinical review. Pediatr Neurol. 2010 Feb; 42(2):77-85.
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  64. Fischer PR, Johnson JN, Boyce TG. Chronic fatigue and infection. Journal of Pediatric Infectious Diseases. 2010; 5(1):1-7.
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  65. Johnson JN, Cetta F. Pericardial Diseases. Pediatric Ultrasound Today. 2010; 4:63-83.
  66. Johnson JN, Ackerman MJ. QTc: how long is too long? Br J Sports Med. 2009 Sep; 43: (9)657-62.
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  67. Kiefer AS, Wickremasinghe AC, Johnson JN, Hartman TK, Hintz SR, Carey WA, Colby CE. Medical management of extremely low-birth-weight infants in the first week of life: a survey of practices in the United States. Am J Perinatol. 2009 Jun; 26(6):407-18. Epub 2009 Mar 19.
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  68. Collura CA, Johnson JN, Moir C, Ackerman MJ. Left cardiac sympathetic denervation for the treatment of long QT syndrome and catecholaminergic polymorphic ventricular tachycardia using video-assisted thoracic surgery. Heart Rhythm. 2009 Jun; 6: (6)752-9.
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  69. Johnson JN, Shaughnessy WJ, Stans AA, Unruh KP, Sim FH, McIntosh AL, Brands CK, Driscoll DJ. Management of knee arthropathy in patients with vascular malformations. J Pediatr Orthop. 2009 Jun; 29(4):380-4.
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  70. Johnson JN, Hartman TK, Barbaresi W, Raffel C, Colby CE. Developmental outcomes for neonatal dural arteriovenous fistulas. J Neurosurg Pediatr. 2009 Feb; 3(2):105-9.
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  71. Johnson JN, Hofman N, Haglund CM, Cascino GD, Wilde AA, Ackerman MJ. Identification of a possible pathogenic link between congenital long QT syndrome and epilepsy. Neurology. 2009 Jan 20; 72: (3)224-31.
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  72. Pianosi PT, Johnson JN, Turchetta A, Johnson BD. Pulmonary function and ventilatory limitation to exercise in congenital heart disease. Congenit Heart Dis. 2009 Jan-Feb; 4(1):2-11.
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  73. Johnson JN, Dhillon RK, Anderson JL. Acute vomiting and mental status changes: a case of acute intraventricular haemorrhage from an optic chiasm tumour. BMJ Case Rep. 2009; 2009:
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  74. Kamath CC, Vickers KS, Ehrlich A, McGovern L, Johnson J, Singhal V, Paulo R, Hettinger A, Erwin PJ, Montori VM. Clinical review: behavioral interventions to prevent childhood obesity: a systematic review and metaanalyses of randomized trials. J Clin Endocrinol Metab. 2008 Dec; 93(12):4606-15. Epub 2008 Sep 09.
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  75. Johnson JN, Hartman TK, Pianosi PT, Driscoll DJ. Cardiorespiratory function after operation for pectus excavatum. J Pediatr. 2008 Sep; 153(3):359-64. Epub 2008 Jun 05.
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  76. Johnson JN, Hartman TK, Krych EH, Seferian EG, Ouellette Y. Tracheomalacia in siblings with otopalatodigital syndrome. Am J Med Genet A. 2008 May 15; 146A(10):1347-9.
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  77. Johnson JN, Tester DJ, Perry J, Salisbury BA, Reed CR, Ackerman MJ. Prevalence of early-onset atrial fibrillation in congenital long QT syndrome. Heart Rhythm. 2008 May; 5: (5)704-9.
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  78. McGovern L, Johnson JN, Paulo R, Hettinger AS, Singhal V, Kamath CC, Erwin PJ, Montori VM. Treatment of Pediatric Obesity. A Systemic Review and Meta-Analysis of Randomized Trials J Clin Endocrinol Metab. 2008; 93(12):4600.